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Benign transient hyperphosphatasemia in juvenile idiopathic arthritis

dc.contributor.authorNeto, A.
dc.contributor.authorNeto, Agna
dc.contributor.authorCosta, M.
dc.contributor.authorBranco, Jaime
dc.contributor.authorBranco, Jaime
dc.contributor.authorMourão, A. F.
dc.contributor.authorMourão, Ana Filipa
dc.contributor.institutionCentro de Estudos de Doenças Crónicas (CEDOC)
dc.contributor.institutionNOVA Medical School|Faculdade de Ciências Médicas (NMS|FCM)
dc.contributor.pblSociedade Portuguesa de Reumatologia
dc.date.accessioned2020-12-30T05:04:03Z
dc.date.available2020-12-30T05:04:03Z
dc.date.issued2019-10-01
dc.description.abstractBenign transient hyperphosphatasemia of infancy and early childhood is a self-limiting condition characte-rized by transiently increased serum alkaline phosphatase in the absence of liver, kidney or metabolic bone diseases. It is often accidentally found in children under five years old and it might be associated with a variety of underlying clinical disorders. Its pathophysiology remains unclear. Herein, we report a case of a 4-year-old girl with a 1-year history of persistent oligoarticular Juvenile Idiopathic Arthritis, who was found to have transient hyperphosphatasemia during a periodic check-up. This clinical case underlines the importance of promptly recognizing this benign condition, which avoids unnecessary extensive investigations.en
dc.description.versionpublishersversion
dc.description.versionpublished
dc.format.extent3
dc.format.extent786242
dc.identifier.issn0303-464X
dc.identifier.otherPURE: 26666768
dc.identifier.otherPURE UUID: 44e82bcb-8cfa-431f-8351-5492387620f4
dc.identifier.otherScopus: 85083544354
dc.identifier.otherPubMed: 32281964
dc.identifier.otherWOS: 000539495400011
dc.identifier.urihttp://hdl.handle.net/10362/109484
dc.identifier.urlhttps://www.scopus.com/pages/publications/85083544354
dc.language.isoeng
dc.peerreviewedyes
dc.subjectHyperphosphatasemia
dc.subjectJuvenile idiopa thic arthritis
dc.subjectRheumatology
dc.titleBenign transient hyperphosphatasemia in juvenile idiopathic arthritisen
dc.title.subtitleA case reporten
dc.typejournal article
degois.publication.firstPage317
degois.publication.issue4
degois.publication.lastPage319
degois.publication.titleActa Reumatológica Portuguesa
degois.publication.volume44
dspace.entity.typePublication
person.familyNameNeto
person.familyNameBranco
person.familyNameMourão
person.givenNameAgna
person.givenNameJaime
person.givenNameAna Filipa
person.identifier.ciencia-idFC1B-7BFA-C219
person.identifier.ciencia-idB612-E5C3-60DC
person.identifier.orcid0000-0002-5681-4674
person.identifier.orcid0000-0001-7024-4375
person.identifier.orcid0000-0002-0299-0963
person.identifier.scopus-author-id8417815400
rcaap.rightsopenAccess
relation.isAuthorOfPublication4621867c-803d-46ce-a923-11e53951df8e
relation.isAuthorOfPublication4caea9f3-40dd-4c95-98ec-0120509287c0
relation.isAuthorOfPublication4a07009b-e53d-460f-8e08-296b80013ef5
relation.isAuthorOfPublication.latestForDiscovery4621867c-803d-46ce-a923-11e53951df8e

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